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KMID : 1103720210820051346
Journal of the Korean Society of Radiology
2021 Volume.82 No. 5 p.1346 ~ p.1351
Osteosarcomatous Transformation in Mazabraud Syndrome: A Case Report
Park Yang-Il

Yoo Ji-Young
Kong Joon-Seog
Abstract
Mazabraud syndrome is a rare benign disease that is accompanied by polyostotic fibrous dysplasia and intramuscular myxoma. Malignant transformation of fibrous dysplasia occurs in approximately 1% of cases. To date, only eight cases of malignant transformation, of fibrous dysplasia to osteosarcoma, in Mazabraud syndrome have been reported worldwide. The authors report the first case of osteosarcomatous transformation in a patient with Mazabraud syndrome in the Republic of Korea, focusing on imaging findings.
KEYWORD
Mazabraud Syndrome, Transformation, Neoplastic Cell, Fibrous Dysplasia of Bone, Myxoma, Osteosarcoma, Magnetic Resonance
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